Unicuspid Aortic Valve
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Cite this case
[...]. Unicuspid Aortic Valve. CTICases. Published December 12, 2014. https://str-case-explorer.pages.dev/c/6fty3
Imaging findings
Retrospectively gated cardiac CT angiography and cine imaging show a severely dilated ascending aorta and a unicuspid aortic valve, which was initially diagnosed as a bicuspid valve on echocardiography.
Key takeaways
A unicuspid aortic valve is the rarest congenital aortic valve anomaly, presenting similarly to a bicuspid valve but typically manifesting earlier in life with severe regurgitation or stenosis, often accompanied by ascending aortic aneurysm.
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