CTICasesPartial Anomalous Pulmonary Venous Return (PAPVR) and Cor Triatriatum Sinister
[...]. Partial Anomalous Pulmonary Venous Return (PAPVR) and Cor Triatriatum Sinister. CTICases. Published March 2, 2017. https://str-case-explorer.pages.dev/c/7gffk
Imaging findings
Chest CT shows an anomalous vein draining all left pulmonary veins and an accessory right middle lobe pulmonary vein into the brachiocephalic vein, representing the extra-cardiac portion of partial anomalous pulmonary venous return. Additionally, the right superior pulmonary vein drains anomalously into the superior vena cava. A large inferior sinus venosus atrial septal defect is noted with an otherwise intact septum primum and secundum. There is a fibromuscular membrane within the left atrium, characteristic of cor triatriatum sinister, and the right heart chambers are significantly enlarged and hypertrophied.
Key takeaways
Partial anomalous pulmonary venous return can be associated with atrial septal defects, specifically sinus venosus defects. Cor triatriatum sinister is a rare congenital anomaly where a membrane partitions the left atrium into two chambers, which can alter normal pulmonary venous flow and exacerbate right heart strain and pulmonary hypertension.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Total Anomalous Pulmonary Venous Return (TAPVR) with Anomalous Systemic Venous Drainage (IVC to Left Atrium)Congenital
- Pulmonary Langerhans Cell Histiocytosis (PLCH)ILD
- Mounier-Kuhn Syndrome (Tracheobronchomegaly) in a Young FemaleCongenital
- Post-CABG Saphenous Vein Graft Pseudoaneurysm and Chest Wall HematomaCoronary
- Mounier-Kuhn Syndrome (Tracheobronchomegaly) in an Elderly Asymptomatic MaleCongenital
- Caseous Calcification of the Mitral Annulus (CCMA) with Pulmonary MAC InfectionValvular
- Left Atrial Appendage (LAA) Thrombus with Embolic StrokeMasses
- Transcatheter Aortic Valve Replacement (TAVR) Complications: Pseudoaneurysm and Valve ThrombosisValvular
See all cases from March 2, 2017 →
Related Congenital cases
- Fontan Palliation Progression for Tricuspid Atresia
- Pulmonary Arteriovenous Malformation with Systemic Collateral Supply
- Azygos Fissure Variant with Superior Intercostal Vein
- Levoatrial Cardinal Vein in Turner Syndrome
- Uncorrected D-Transposition of the Great Arteries
- Congenitally Corrected Transposition of the Great Arteries (L-TGA) with Situs Inversus