CTICasesTetralogy of Fallot with pulmonary atresia and MAPCAs
[...]. Tetralogy of Fallot with pulmonary atresia and MAPCAs. CTICases. Published September 26, 2019. https://str-case-explorer.pages.dev/c/86fhv
Imaging findings
CT angiogram of a 3-week-old cyanotic newborn shows Tetralogy of Fallot with severe RV hypertrophy, VSD, and a hypoplastic/atretic RV outflow tract. Multiple large systemic collateral arteries (MAPCAs) arise from the descending aorta to supply the pulmonary parenchyma.
Key takeaways
Major aortopulmonary collateral arteries (MAPCAs) are congenital vessels that develop in the setting of severe pulmonary outflow tract obstruction (such as Tetralogy of Fallot with pulmonary atresia) to supply the lungs. Surgical management requires unifocalisation to connect collaterals to a reconstructed pulmonary trunk.
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