CTICasesGorham-Stout Disease (Generalized Lymphatic Anomaly) with Bony Anomalies
[...]. Gorham-Stout Disease (Generalized Lymphatic Anomaly) with Bony Anomalies. CTICases. Published September 23, 2016. https://str-case-explorer.pages.dev/c/bngvv
Imaging findings
The patient has scattered, unusual-looking sclerotic bony lesions in the sternum and ribs (chest CT not available in the transcript, but mentioned). An older study shows a large, multiloculated cystic collection in the left upper and lower abdomen. MRI reveals the L5 vertebral body is filled with a similar multiloculated cystic structure. The large lymphangioma in the bone required surgical correction.
Key takeaways
Gorham-Stout disease, or generalized lymphatic anomaly, is a rare condition characterized by the proliferation of lymphatic channels, often involving bone and soft tissues. It can lead to osteolysis ('vanishing bone disease') and present with multiloculated cystic lymphatic malformations. The bony anomalies are associated with lymphatic channels traversing the bones. Surgical intervention may be necessary for large or symptomatic lesions.
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