CTICasesBronchopulmonary Sequestration with Bronchial Atresia
[...]. Bronchopulmonary Sequestration with Bronchial Atresia. CTICases. Published April 14, 2018. https://str-case-explorer.pages.dev/c/dsprb
Imaging findings
CT of the right lung base shows a bubbly lesion with a large component of emphysema, unusual bronchial-appearing elements in its center, and a systemic artery arising from the descending aorta that enhances on contrast-enhanced imaging and supplies the lesion. A coronal reformat highlights a distinctly bronchial branching pattern within the lesion that could not be traced back to a connection with the native airway. The lesion was resected and pathology described cysts lined by bronchial epithelium/endothelium, with surrounding emphysema centered on a denser nidus.
Key takeaways
This was an unusually well-formed example of pulmonary sequestration showing true bronchial branching rather than simple cysts, likely representing a hybrid lesion. There is a well-recognized association between sequestration, bronchial atresia, and congenital lobar overinflation because all three can arise from the same disrupted lung bud: airway remnants that never connect, vascular remnants that fail to regress, and parenchyma that develops abnormally.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Intra-arterial Pulmonary Metastases from ChondrosarcomaNeoplastic
- Paget-Schroetter Syndrome (Effort Thrombosis of the Subclavian Vein)Vascular
- Loeys-Dietz SyndromeAorta & Arteries
- Cervical Aortic Arch with Aberrant Subclavian Artery in DiGeorge SyndromeAorta & Arteries
- Anti-Jo-1 Antisynthetase SyndromeILD
- Anti-PL-7 Antisynthetase SyndromeILD
- Solitary Pulmonary AmyloidomaMetabolic
- Brown Tumors from Renal Osteodystrophy (Secondary Hyperparathyroidism)Metabolic
See all cases from April 14, 2018 →
Related Congenital cases
- Azygos Continuation of the IVC with Bilateral Hyparterial Bronchi and Polysplenia-like Anatomy
- Primary Ciliary Dyskinesia (Kartagener Syndrome) with Situs Inversus and Bronchiectasis
- Left Pre-hyparterial Accessory Bronchus
- Anomalous Systemic Arterial Supply to the Right Lower Lobe
- Cor Triatriatum Sinister with Levoatrial Cardinal Vein
- Non-Obstructive Cor Triatriatum Sinister