Pulmonary Artery Sling with Tracheal Anomalies
[...]. Pulmonary Artery Sling with Tracheal Anomalies. CTICases. Published December 10, 2020. https://str-case-explorer.pages.dev/c/sk8dp
Imaging findings
A woman in her 70s with no prior documentation has a pulmonary artery sling with an abnormally small trachea that may contain complete cartilaginous rings, a persistent left SVC (duplicated SVC), and an unusual low-lying, abnormally branching carina suggesting left isomerism.
Key takeaways
A type 2 pulmonary artery sling is associated with airway anomalies such as complete tracheal rings, tracheal narrowing, and abnormal branching (here suggesting left isomerism). This vascular-airway combination can rarely go undiagnosed into the eighth decade when the tracheal stenosis is modest, and it may be discovered de novo in an adult.
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