CTICasesHybrid Congenital Lesion: CPAM, Sequestration, and Bronchial Atresia
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[...]. Hybrid Congenital Lesion: CPAM, Sequestration, and Bronchial Atresia. CTICases. Published January 14, 2016. https://str-case-explorer.pages.dev/c/79w2r
Imaging findings
The lesion appears as a bubbly cystic mass, consistent with a CPAM. It also features a large, single feeding artery originating from the systemic circulation, characteristic of a sequestration. Additionally, there is evidence of bronchial atresia, with normal proximal airways disappearing, and abnormal, blind-ending tubular structures in the region trying to reach the hilum, potentially containing mucus.
Key takeaways
This is a rare 'trilogy' of congenital lesions, combining features of CPAM, sequestration, and bronchial atresia within a single lesion. While CPAM features in sequestrations are often seen, the combination with bronchial atresia is less commonly reported in literature, suggesting an entire spectrum of congenital airway and sequestration abnormalities. The presence of a large systemic feeding artery differentiates it from an acquired vessel.
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