CTICasesWilliams-Campbell syndrome
[...]. Williams-Campbell syndrome. CTICases. Published October 26, 2019. https://str-case-explorer.pages.dev/c/d26j5
Imaging findings
CT scan of a 56-year-old male with chronic cough shows severe, symmetric cystic bronchiectasis involving the segmental and subsegmental bronchi, with sparing of the trachea and main bronchi. Left lower lobectomy pathology confirmed a developmental deficiency of bronchial cartilage.
Key takeaways
Williams-Campbell syndrome is a rare congenital disorder characterized by a deficiency of cartilage in the sublobar (segmental and subsegmental) bronchi, leading to bronchiectasis, airway collapse during expiration, and recurrent infections.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Pulmonary veno-occlusive disease (PVOD) in mixed connective tissue diseaseVascular
- Ascending aortic pseudoaneurysm secondary to sternal wound infectionAorta & Arteries
- Septal emboli and spinal discitis/osteomyelitis with paravertebral abscessInfection
- Excipient lung disease (talc granulomatosis)Exposure
- Disseminated Mycobacterium avium complex (MAC) in HIVInfection
- Excipient lung disease secondary to oral painkiller abuseExposure
- Pectus excavatum mimicking right middle/lower lobe pneumonia (pseudo-pneumonia)Artifact
- Invasive Klebsiella syndrome with hepatic abscesses and necrotizing pneumoniaInfection
See all cases from October 26, 2019 →
Related Congenital cases
- Unrepaired sinus venosus ASD and PAPVR in a heart transplant recipient
- Pulmonary vascular telangiectasias in sickle cell disease
- Tetralogy of Fallot with pulmonary atresia and MAPCAs
- Large mediastinal thymic cyst
- Systemic arterial supply to normal lung without sequestration
- Superior sinus venosus ASD and PAPVR